Bacillus Calmette–Guérin (BCG)‐associated hemophagocytic lymphohistiocytosis in the setting of IFN‐γR1 deficiency: A diagnostic dilemma
Abstract Hemophagocytic lymphohistiocytosis (HLH) disease is a severe immune dysregulation caused by mutations in genes required for lymphocyte cytotoxicity function. However, HLH‐like syndrome may develop secondary to infections, malignancy, and autoimmunity. Primary immunodeficiencies (PIDs) could...
Main Authors: | , , , , , , |
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Format: | Article |
Language: | English |
Published: |
Wiley
2020-07-01
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Series: | eJHaem |
Online Access: | https://doi.org/10.1002/jha2.5 |