Bacillus Calmette–Guérin (BCG)‐associated hemophagocytic lymphohistiocytosis in the setting of IFN‐γR1 deficiency: A diagnostic dilemma

Abstract Hemophagocytic lymphohistiocytosis (HLH) disease is a severe immune dysregulation caused by mutations in genes required for lymphocyte cytotoxicity function. However, HLH‐like syndrome may develop secondary to infections, malignancy, and autoimmunity. Primary immunodeficiencies (PIDs) could...

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Bibliographic Details
Main Authors: Anahita Razaghian, Leila Parvaneh, Mona Delkhah, Arash Abbasi, Parisa Sadeghirad, Mohammad Shahrooei, Nima Parvaneh
Format: Article
Language:English
Published: Wiley 2020-07-01
Series:eJHaem
Online Access:https://doi.org/10.1002/jha2.5