Dietary Management of the Ketogenic Glycogen Storage Diseases
The glycogen storage diseases (GSDs) comprise a group of rare inherited disorders of glycogen metabolism. The hepatic glycogenolytic forms of these disorders are typically associated with hypoglycemia and hepatomegaly. For GSD I, secondary metabolic disturbances include fasting hyperlactatemia, hype...
| Main Authors: | , , |
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| Format: | Article |
| Language: | English |
| Published: |
SciELO
2016-08-01
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| Series: | Journal of Inborn Errors of Metabolism and Screening |
| Online Access: | https://doi.org/10.1177/2326409816661359 |