Strong inflammatory signatures in the neutrophils of PAMI syndrome

PSTPIP1 (proline-serine-threonine phosphatase-interactive protein 1)–associated myeloid-related proteinemia inflammatory (PAMI) syndrome is a rare autoinflammatory disease caused by heterozygous gain-of-function mutation in PSTPIP1. As one of the PSTPIP1-associated inflammatory diseases (PAIDs), neu...

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Bibliographic Details
Main Authors: Wenjie Zheng, Xiaorui Fan, Zhaohui Yang, Yaoyao Shangguan, Taijie Jin, Yan Liu, Jiqian Huang, Xiaohua Ye, Qing Zhou, Xiaozhong Li
Format: Article
Language:English
Published: Frontiers Media S.A. 2022-09-01
Series:Frontiers in Immunology
Subjects:
Online Access:https://www.frontiersin.org/articles/10.3389/fimmu.2022.926087/full