Management of suspected monogenic lung fibrosis in a specialised centre
At least 10% of patients with interstitial lung disease present monogenic lung fibrosis suspected on familial aggregation of pulmonary fibrosis, specific syndromes or early age of diagnosis. Approximately 25% of families have an identified mutation in genes mostly involved in telomere homeostasis, a...
| Main Authors: | , , , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
European Respiratory Society
2017-04-01
|
| Series: | European Respiratory Review |
| Online Access: | http://err.ersjournals.com/content/26/144/160122.full |