Lung function decline preceding chronic respiratory failure in spinal muscular atrophy: a national prospective cohort study

Lung function decline preceding chronic respiratory failure in spinal muscular atrophy: a national prospective cohort study

Abstract Background Progressive lung function decline, resulting in respiratory failure, is an important complication of spinal muscular atrophy (SMA). The ability to predict the need for mechanical ventilation is important. We assessed longitudinal patterns of lung function prior to chronic respira...

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Main Authors: Esther S. Veldhoen, Camiel A. Wijngaarde, Ruben P. A. van Eijk, Fay-Lynn Asselman, Negina Seddiqi, Louise A. M. Otto, Marloes Stam, Inge Cuppen, Renske I. Wadman, Roelie M. Wösten van Asperen, Erik H. J. Hulzebos, Laura P. Verweij van den Oudenrijn, Bart Bartels, Jasmijn Boezer, M. Gaytant, Cornelis K. van der Ent, W. Ludo van der Pol
Format: Article
Language:English
Published: BMC 2023-02-01
Series:Orphanet Journal of Rare Diseases
Subjects:
Lung function
Natural history
Neuromuscular
Respiratory failure
Spinal muscular atrophy
Online Access:https://doi.org/10.1186/s13023-023-02634-4

Internet

https://doi.org/10.1186/s13023-023-02634-4

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