Mitochondrial Fatty Acid Beta-Oxidation Disorders in Children: Literature Review

Congenital mitochondrial fatty acid beta-oxidation disorders are a heterogeneous group of metabolic disorders characterized by impaired fatty acid metabolism in mitochondria. It results in central nervous system, skeletal muscle, cardiovascular system, and liver damage, as well as the development of...

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Bibliographic Details
Main Authors: Natalia V. Zhurkova, Nato V. Vashakmadze, Andrey N. Surkov, Olga Ya. Smirnova, Natalia S. Sergienko, Natallia G. Ovsyanik, Lilia R. Selimzyanova
Format: Article
Language:English
Published: "Paediatrician" Publishers LLC 2023-01-01
Series:Вопросы современной педиатрии
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Online Access:https://vsp.spr-journal.ru/jour/article/view/3089