Mitochondrial Fatty Acid Beta-Oxidation Disorders in Children: Literature Review
Congenital mitochondrial fatty acid beta-oxidation disorders are a heterogeneous group of metabolic disorders characterized by impaired fatty acid metabolism in mitochondria. It results in central nervous system, skeletal muscle, cardiovascular system, and liver damage, as well as the development of...
Main Authors: | , , , , , , |
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Format: | Article |
Language: | English |
Published: |
"Paediatrician" Publishers LLC
2023-01-01
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Series: | Вопросы современной педиатрии |
Subjects: | |
Online Access: | https://vsp.spr-journal.ru/jour/article/view/3089 |