Application of Forced Oscillation Technique in Assessing Pulmonary Fibrosis in Hermansky–Pudlak Syndrome

Application of Forced Oscillation Technique in Assessing Pulmonary Fibrosis in Hermansky–Pudlak Syndrome

Hermansky–Pudlak syndrome (HPS) is a rare autosomal recessive disorder characterized by defects in lysosome-related organelles. Given the high mortality rate associated with HPS pulmonary fibrosis (PF) and the significant risks tied to lung transplantation, it is essential to explore new tools for t...

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Bibliographic Details
Main Authors: Wilfredo De Jesús-Rojas, Luis Reyes-Peña, José Muñiz-Hernandez, Rolando Mena-Ventura, Gabriel Camareno-Soto, Gabriel Rosario-Ortiz, Marcos J. Ramos-Benitez, Monica Egozcue-Dionisi, Enid Rivera-Jimenez, Rosa Román-Carlo
Format: Article
Language:English
Published: MDPI AG 2024-10-01
Series:Advances in Respiratory Medicine
Subjects:
forced oscillation technique
pulmonary fibrosis
Hermansky–Pudlak syndrome
respiratory mechanics
Online Access:https://www.mdpi.com/2543-6031/92/6/40

Internet

https://www.mdpi.com/2543-6031/92/6/40

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