Síndrome de Prune Belly com fístula vesicocutânea: relato de caso raro e revisão da literatura

Prune Belly syndrome (PBS) is a rare complex malformation that preferentially affects male newborns. It presents with a wide spectrum of alterations that include abdominal muscle deficiency, varying degrees of renal dysplasia and urinary tract obstruction, in addition to bilateral cryptorchidism. In...

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Bibliographic Details
Main Authors: Debora Leticia Silva Gouvêa Viana, Naara Rafaela Gonçalves, Álvaro Henrique Anghietti Nalon, Michel Correia Viana, Rúbia Cecília Barbone e Melo, Ítalo Guilherme Giarola de Freitas Mariano, Raquel Ida Ferreira, Thais Silva Maia, Paula Silva Maia
Format: Article
Language:English
Published: Sociedade Brasileira de Pediatria 2023-12-01
Series:Residência Pediátrica
Subjects:
Online Access:https://cdn.publisher.gn1.link/residenciapediatrica.com.br/pdf/v13n4e696.pdf