Lymphangioleiomyomatosis: what do we know and what are we looking for?
Lymphangioleiomyomatosis (LAM) is a rare disease characterised by proliferation of abnormal smooth muscle-like cells (LAM cells) leading to progressive cystic destruction of the lung, lymphatic abnormalities and abdominal tumours. It affects predominantly females and can occur sporadically or in pat...
Main Authors: | , , |
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Format: | Article |
Language: | English |
Published: |
European Respiratory Society
2011-03-01
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Series: | European Respiratory Review |
Subjects: | |
Online Access: | http://err.ersjournals.com/content/20/119/034.full.pdf+html |