Gingival Hypertrophy in a Child with Hyaline Fibromatosis Syndrome

Hyaline fibromatosis syndrome (HFS) is a rare autosomal recessive genetic disorder characterized by accumulation of hyalinized fibrous tissue with cutaneous, mucosal, osteoarticular, and systemic involvement. The condition is caused by a mutation of ANTXR2 gene that results in a faulty synthesis of...

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Bibliographic Details
Main Authors: Predrag Knežević, Marko Tarle, Lucija Ida Fratrić, Antonia Tarle, Hana Knežević-Krajina, Darko Macan
Format: Article
Language:English
Published: University of Zagreb. School of Dental Medicine 2020-01-01
Series:Acta Stomatologica Croatica
Subjects:
Online Access:https://hrcak.srce.hr/file/342469