Total and reduced/oxidized forms of coenzyme Q10 in fibroblasts of patients with mitochondrial disease

Total and reduced/oxidized forms of coenzyme Q10 in fibroblasts of patients with mitochondrial disease

Coenzyme Q10 (CoQ10) is involved in ATP production through electron transfer in the mitochondrial respiratory chain complex. CoQ10 receives electrons from respiratory chain complex I and II to become the reduced form, and then transfers electrons at complex III to become the oxidized form. The redox...

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Bibliographic Details
Main Authors: Chika Watanabe, Hitoshi Osaka, Miyuki Watanabe, Akihiko Miyauchi, Eriko F. Jimbo, Takeshi Tokuyama, Hideki Uosaki, Yoshihito Kishita, Yasushi Okazaki, Takanori Onuki, Tomohiro Ebihara, Kenichi Aizawa, Kei Murayama, Akira Ohtake, Takanori Yamagata
Format: Article
Language:English
Published: Elsevier 2023-03-01
Series:Molecular Genetics and Metabolism Reports
Subjects:
Mitochondrial disease
Primary coenzyme Q10 deficiency
Coenzyme Q10
Reduced/total CoQ10
Forward electron transport
Reverse electron transport
Online Access:http://www.sciencedirect.com/science/article/pii/S2214426922001112

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http://www.sciencedirect.com/science/article/pii/S2214426922001112

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