Presentation and progression of MPO-ANCA interstitial lung disease

The association between MPO-ANCA-associated vasculitis (AAV) and interstitial lung disease (ILD) has been well established. Pulmonary fibrosis may coexist with, follow, or even precede the diagnosis of AAV, and its presence adversely affects the prognosis. The optimal approach to investigating ANCA...

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Main Authors: Lorenzo Salvati, Boaz Palterer, Elena Lazzeri, Emanuele Vivarelli, Marina Amendola, Marco Allinovi, Leonardo Caroti, Alessio Mazzoni, Laura Lasagni, Giacomo Emmi, Edoardo Cavigli, Marco Del Carria, Linda Di Pietro, Mariangela Scavone, Daniele Cammelli, Federico Lavorini, Sara Tomassetti, Elisabetta Rosi, Paola Parronchi
Format: Article
Language:English
Published: Elsevier 2024-06-01
Series:Journal of Translational Autoimmunity
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2589909024000054