Epstein–Barr virus-related hemophagocytic lymphohistiocytosis complicated with coronary artery dilation and acute renal injury in a boy with a novel X-linked inhibitor of apoptosis protein (XIAP) variant: a case report

Epstein–Barr virus-related hemophagocytic lymphohistiocytosis complicated with coronary artery dilation and acute renal injury in a boy with a novel X-linked inhibitor of apoptosis protein (XIAP) variant: a case report

Abstract Background X-linked lymphoproliferative disease (XLP) is a rare inherited X-linked primary immunodeficiency diseases (PID). One such disease, X-linked inhibitor of apoptosis protein (XIAP) deficiency, is characterized by Epstein–Barr virus-related hemophagocytic lymphohistiocytosis (EBV-HLH...

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Bibliographic Details
Main Authors: Ru-Yue Chen, Xiao-Zhong Li, Qiang Lin, Yun Zhu, Yun-Yan Shen, Qin-Ying Xu, Xue-Ming Zhu, Zhen-Jiang Bai, Ying Li
Format: Article
Language:English
Published: BMC 2020-10-01
Series:BMC Pediatrics
Subjects:
X-linked inhibitor of apoptosis protein (XIAP)
Hemophagocytic lymphohistiocytosis (HLH)
Epstein–Barr virus (EBV)
Coronary artery dilatation
Acute renal injury (AKI)
Online Access:http://link.springer.com/article/10.1186/s12887-020-02359-4

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http://link.springer.com/article/10.1186/s12887-020-02359-4

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