Long-term clinical course and outcomes in patients with lymphangioleiomyomatosis

Long-term clinical course and outcomes in patients with lymphangioleiomyomatosis

Abstract Background Lymphangioleiomyomatosis (LAM) is a rare multisystemic disorder with various clinical manifestations. Despite the recognition of several prognostic factors, the long-term clinical course and prognosis of patients with LAM in the era of sirolimus therapy are not established. Metho...

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Bibliographic Details
Main Authors: Hee-Young Yoon, Ho Jeong Kim, Jin Woo Song
Format: Article
Language:English
Published: BMC 2022-06-01
Series:Respiratory Research
Subjects:
Lymphangioleiomyomatosis
Prognosis
Respiratory function test
Patient outcome assessment
Rare diseases
Online Access:https://doi.org/10.1186/s12931-022-02079-6

Internet

https://doi.org/10.1186/s12931-022-02079-6

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