Lung Inflammatory Genes in Cystic Fibrosis and Their Relevance to Cystic Fibrosis Transmembrane Conductance Regulator Modulator Therapies
Cystic fibrosis (CF) is a monogenic syndrome determined by over 2000 mutations in the <i>CF Transmembrane Conductance Regulator</i> (<i>CFTR</i>) gene harbored on chromosome 7. In people with CF (PWCF), lung disease is the major determinant of morbidity and mortality and is c...
Main Authors: | Annalucia Carbone, Pamela Vitullo, Sante Di Gioia, Massimo Conese |
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Format: | Article |
Language: | English |
Published: |
MDPI AG
2023-10-01
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Series: | Genes |
Subjects: | |
Online Access: | https://www.mdpi.com/2073-4425/14/10/1966 |
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