The fibrogenic chemokine CCL18 is associated with disease severity in Erdheim-Chester disease

Erdheim-Chester disease (ECD) is a rare histiocytosis, characterized by xanthogranulomatous tissue infiltration by foamy histiocytes. Fibrosis, a histologic hallmark of ECD, is responsible for lesion growth and clinical manifestations. Unraveling molecular fibrotic pathway in ECD would allow the ide...

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Bibliographic Details
Main Authors: Greta Pacini, Giulio Cavalli, Alessandro Tomelleri, Giacomo De Luca, Guido Pacini, Marina Ferrarini, Claudio Doglioni, Lorenzo Dagna
Format: Article
Language:English
Published: Taylor & Francis Group 2018-07-01
Series:OncoImmunology
Subjects:
Online Access:http://dx.doi.org/10.1080/2162402X.2018.1440929