How I manage pulmonary Langerhans cell histiocytosis
Pulmonary Langerhans cell histiocytosis (PLCH) is a rare sporadic cystic lung disease of unknown aetiology that is characterised by the infiltration and destruction of the wall of distal bronchioles by CD1a+ Langerhans-like cells. In adults, PLCH is frequently isolated and affects young smokers of b...
Main Authors: | , |
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Format: | Article |
Language: | English |
Published: |
European Respiratory Society
2017-09-01
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Series: | European Respiratory Review |
Online Access: | http://err.ersjournals.com/content/26/145/170070.full |