Case Report: Evolution of a Severe Vascular Refractory Form of ECD Requiring Liver Transplantation Correlated With the Change in the Monocyte Subset Analysis

Case Report: Evolution of a Severe Vascular Refractory Form of ECD Requiring Liver Transplantation Correlated With the Change in the Monocyte Subset Analysis

Erdheim–Chester disease is a rare histiocytosis characterized by iconic features associated with compatible histology. Most patients have somatic mutations in the MAP-kinase pathway gene, and the mutations occur in CD14+ monocytes. Differentiation of the myeloid lineage plays a central role in the p...

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Bibliographic Details
Main Authors: Jérôme Razanamahery, Anne Roggy, Jean-François Emile, Alexandre Malakhia, Zaher Lakkis, Francine Garnache-Ottou, Thibaud Soumagne, Fleur Cohen-Aubart, Julien Haroche, Bernard Bonnotte
Format: Article
Language:English
Published: Frontiers Media S.A. 2021-11-01
Series:Frontiers in Immunology
Subjects:
monocyte
histiocytosis
Erdheim–Chester disease
transplantation
vascular diagnosis
Online Access:https://www.frontiersin.org/articles/10.3389/fimmu.2021.755846/full

Internet

https://www.frontiersin.org/articles/10.3389/fimmu.2021.755846/full

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