A Suspected Case of Cerebral Fat Embolism Triggering a Drug-resistant Status Epilepticus in a HbS/β⁺-Thalassaemia Patient

Sickle cell disease (SCD) refers to a group of hereditary disorders associated with clinical manifestations of variable severity. C In particular, Fat Embolism Syndrome, a rare and devastating complication of SCD, may preferentially involve non-homozygous patients and patients with mild disease. 

Bibliographic Details
Main Authors: Marta Bortolotti, Gianluca Costamagna, Marta Mancarella, Delia Gagliardi, Silvia Lanfranconi, Alessia Marcon, Margherita Migone De Amicis, Nereo Bresolin, Stefania Corti, Giovanna Graziadei
Format: Article
Language:English
Published: PAGEPress Publications 2022-02-01
Series:Mediterranean Journal of Hematology and Infectious Diseases
Subjects:
Online Access:http://mjhid.org/index.php/mjhid/article/view/4805