Rare gynecological entity: malignant cervical PEComa (perivascular epithelioid cell differentiation tumour) - challenges in diagnosis, treatment and surveillance

Perivascular epithelioid cell tumors constitute a family of mesenchymal tumors characterized by the concomitant expression of melanocytic and muscular markers. Gynecological perivascular epithelioid cell tumors are rare, encompassing about 25% of cases. Studies demonstrate an even rarer occurrence i...

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Bibliographic Details
Main Authors: Amanda da Silva Anjos, Filipe Vieira Kwiatkowski, Rafael Vieira Kwiatkowski, Danielle Rediess Bonow, Luana Ferreira Vasques, Sabine Triguero Teixeira
Format: Article
Language:English
Published: Sociedade Brasileira de Oncologia Clínica, Sociedade Brasileira de Cirurgia Clínica and Sociedade Brasileira de Radioterapia 2024-05-01
Series:Brazilian Journal of Oncology
Subjects:
Online Access:https://www.brazilianjournalofoncology.com.br/details/276/en-US/rare-gynecological-entity--malignant-cervical-pecoma--perivascular-epithelioid-cell-differentiation-tumour----challenges-in-diagnosis--treatment-and-s