Thrombotic microangiopathy in children: Redefining hemolytic uremic syndrome, thrombotic thrombocytopenic purpura and related disorders
Thrombotic microangiopathy (TMA) is a triad of microangiopathic hemolytic anemia, thrombocytopenia, and end-organ ischemic damage. The primary mechanism involved is the occurrence of microthrombi due to deficient activity of ADAMTS13 (A Disintegrin And Metalloprotease with ThromboSpondin type 1 repe...
Main Authors: | , |
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Format: | Article |
Language: | English |
Published: |
Elsevier
2024-03-01
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Series: | Pediatric Hematology Oncology Journal |
Subjects: | |
Online Access: | http://www.sciencedirect.com/science/article/pii/S2468124524000056 |