Primary familial and congenital polycythemia; The forgotten entity
Primary familial and congenital polycythemia (PFCP) is a rare autosomal dominant disorder caused by hypersensitivity of erythropoietin receptor of erythroid progenitors leading to increased rate of erythropoiesis at any given serum erythropoietin level. The hallmark of this disorder is isolated eryt...
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Format: | Article |
Language: | English |
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Wolters Kluwer Medknow Publications
2018-01-01
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Series: | Journal of Applied Hematology |
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Online Access: | http://www.jahjournal.org/article.asp?issn=1658-5127;year=2018;volume=9;issue=2;spage=39;epage=44;aulast=Aljabry |