Systematic review of the incidence and clinical risk predictors of atrial fibrillation and permanent pacemaker implantation for bradycardia in Fabry disease

Introduction Fabry disease (FD) is an X-linked lysosomal storage disorder caused by enzyme deficiency, leading to glycosphingolipid accumulation. Cardiac accumulation triggers local tissue injury, electrical instability and arrhythmia. Bradyarrhythmia and atrial fibrillation (AF) incidence are repor...

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Bibliographic Details
Main Authors: Ravi Vijapurapu, Derralynn A Hughes, Tarekegn Geberhiwot, Richard Paul Steeds, Dipak Kotecha, Adrian Warfield, James Moon, Peter Woolfson, Polyvios Demetriades, Ashwin Roy, Joseph de Bono
Format: Article
Language:English
Published: BMJ Publishing Group 2023-11-01
Series:Open Heart
Online Access:https://openheart.bmj.com/content/10/2/e002316.full