Fulfillment status of hypertriglyceridemia and hypofibrinogenemia in children with hemophagocytic lymphohistiocytosis and risks of multiple organ dysfunction syndrome and early mortality

Fulfillment status of hypertriglyceridemia and hypofibrinogenemia in children with hemophagocytic lymphohistiocytosis and risks of multiple organ dysfunction syndrome and early mortality

Abstract Background Hemophagocytic lymphohistiocytosis (HLH) is a life-threatening disorder. How to stratify high risk patients is one of the current challenges for the treatment of HLH. HLH patients usually fulfill multiple but not all eight diagnostic criteria. Different combinations of the fulfil...

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Bibliographic Details
Main Authors: Xun Li, Haipeng Yan, Ting Luo, Zhenghui Xiao, Ling Gong, Jiaotian Huang, Xinping Zhang, Mincui Zheng, Zhenya Yao, Ping Zang, Desheng Zhu, Xiulan Lu
Format: Article
Language:English
Published: BMC 2022-04-01
Series:Orphanet Journal of Rare Diseases
Subjects:
Child
Fibrinogen
Multiple organ dysfunction syndrome
Hemophagocytic lymphohistiocytosis
Triglyceride
Online Access:https://doi.org/10.1186/s13023-022-02315-8

Internet

https://doi.org/10.1186/s13023-022-02315-8

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