Alveolar proteinosis of genetic origins
Pulmonary alveolar proteinosis (PAP) is a rare form of chronic interstitial lung disease, characterised by the intra-alveolar accumulation of lipoproteinaceous material. Numerous conditions can lead to its development. Whereas the autoimmune type is the main cause in adults, genetic defects account...
| Main Authors: | , , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
European Respiratory Society
2020-10-01
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| Series: | European Respiratory Review |
| Online Access: | http://err.ersjournals.com/content/29/158/190187.full |