Use of elexacaftor+tezacaftor+ivacaftor in individuals with cystic fibrosis and at least one F508del allele: a systematic review and meta-analysis

ABSTRACT Objective: To evaluate the effect of treatment with the combination of three cystic fibrosis transmembrane conductance regulator (CFTR) modulators-elexacaftor+tezacaftor+ivacaftor (ETI)-on important clinical endpoints in individuals with cystic fibrosis. Methods: This was a systematic rev...

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Bibliographic Details
Main Authors: Luiz Vicente Ribeiro Ferreira da Silva Filho, Rodrigo Abensur Athanazio, Carolina Rodrigues Tonon, Juliana Carvalho Ferreira, Suzana Erico Tanni
Format: Article
Language:English
Published: Sociedade Brasileira de Pneumologia e Tisiologia 2024-01-01
Series:Jornal Brasileiro de Pneumologia
Subjects:
Online Access:http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1806-37132023000601201&tlng=en