Perioperative care of a child with Zellweger syndrome.
Zellweger syndrome (ZS) is an autosomal recessive dis- order characterized by defects in the structure, function, or number of peroxisomes, which are essential for the β- oxidation of very-long-chain fatty acids. Disordered pe- roxisome function leads to a wide range of metabolic ab- normalities and...
Main Authors: | , |
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Format: | Article |
Language: | English |
Published: |
Pediatric Anesthesia and Critical Care Journal
2022-08-01
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Series: | Pediatric Anesthesia and Critical Care Journal (PACCJ) |
Subjects: | |
Online Access: | http://www.anestesiarianimazione.com/PACCJ%202022/Perioperative%20care%20of%20a%20child%20with%20Zellweger%20syndrome.pdf |