Liver Assessment in Patients with Ataxia-Telangiectasia: Transient Elastography Detects Early Stages of Steatosis and Fibrosis

Background. Ataxia-telangiectasia (A-T) is a rare autosomal-recessive multisystem disorder characterized by pronounced cerebellar ataxia, telangiectasia, cancer predisposition, and altered body composition. Liver diseases with steatosis, fibrosis, and hepatocellular carcinoma are frequent findings i...

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Detalhes bibliográficos
Principais autores: H. Donath, S. Wölke, V. Knop, U. Heß, R. P. Duecker, J. Trischler, T. Poynard, R. Schubert, S. Zielen
Formato: Artigo
Idioma:English
Publicado em: Hindawi Limited 2023-01-01
coleção:Canadian Journal of Gastroenterology and Hepatology
Acesso em linha:http://dx.doi.org/10.1155/2023/2877350