Liver Assessment in Patients with Ataxia-Telangiectasia: Transient Elastography Detects Early Stages of Steatosis and Fibrosis

Background. Ataxia-telangiectasia (A-T) is a rare autosomal-recessive multisystem disorder characterized by pronounced cerebellar ataxia, telangiectasia, cancer predisposition, and altered body composition. Liver diseases with steatosis, fibrosis, and hepatocellular carcinoma are frequent findings i...

Full description

Bibliographic Details
Main Authors: H. Donath, S. Wölke, V. Knop, U. Heß, R. P. Duecker, J. Trischler, T. Poynard, R. Schubert, S. Zielen
Format: Article
Language:English
Published: Hindawi Limited 2023-01-01
Series:Canadian Journal of Gastroenterology and Hepatology
Online Access:http://dx.doi.org/10.1155/2023/2877350

Similar Items