Liver Assessment in Patients with Ataxia-Telangiectasia: Transient Elastography Detects Early Stages of Steatosis and Fibrosis
Background. Ataxia-telangiectasia (A-T) is a rare autosomal-recessive multisystem disorder characterized by pronounced cerebellar ataxia, telangiectasia, cancer predisposition, and altered body composition. Liver diseases with steatosis, fibrosis, and hepatocellular carcinoma are frequent findings i...
Main Authors: | H. Donath, S. Wölke, V. Knop, U. Heß, R. P. Duecker, J. Trischler, T. Poynard, R. Schubert, S. Zielen |
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Format: | Article |
Language: | English |
Published: |
Hindawi Limited
2023-01-01
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Series: | Canadian Journal of Gastroenterology and Hepatology |
Online Access: | http://dx.doi.org/10.1155/2023/2877350 |
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