Successful induction therapy with sequential CVD followed by high-dose lanreotide in for metastatic SDHB paraganglioma: Case report

Objective: Pheochromocytomas (PHEOs) and paragangliomas (PGLs) arise from adrenal extra-adrenal paraganglia. They often secrete catecholamine and approximately 1/3 are hereditary. Almost 50% of metastatic PGLs are caused by mutations in the succinate dehydrogenase gene, particularly in subunits B an...

Full description

Bibliographic Details
Main Authors: Isabel Tena, José Luis Ponce, Marcos Tajahuerce, José Luis Vercher-Conejero, Manuel Cifrián, Katherine I. Wolf, Marcela Miret, Maribel del Olmo, Rosa Reboll, Antonio Conde, Francisca Moreno, Julia Balaguer, Adela Cañete, Rosana Palasí, Alfredo Marco, Juan Francisco Merino Torres, Carlos Ferrer, Alfredo Sánchez, José Luis Soto, Antonio Llombart, Karel Pacak
Format: Article
Language:English
Published: Elsevier 2018-03-01
Series:Journal of Clinical and Translational Endocrinology Case Reports
Online Access:http://www.sciencedirect.com/science/article/pii/S2214624517300151