The Effect of a Fat-Restricted Diet in Four Patients with Familial Chylomicronemia Syndrome: A Long-Term Follow-Up Study

The Effect of a Fat-Restricted Diet in Four Patients with Familial Chylomicronemia Syndrome: A Long-Term Follow-Up Study

(1) Background: Familial chylomicronemia syndrome (FCS) is a very rare autosomal recessive disorder characterized by severely elevated triglycerides and clinical symptoms in early childhood mainly presenting with abdominal pain, acute pancreatitis and hepatosplenomegaly. Primary treatment is a lifel...

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Bibliographic Details
Main Authors: Alexandra Thajer, Gabriele Skacel, Charlotte de Gier, Susanne Greber-Platzer
Format: Article
Language:English
Published: MDPI AG 2021-11-01
Series:Children
Subjects:
familial chylomicronemia syndrome
FCS traffic light table
dietary management
lipoprotein lipase deficiency
primary chylomicronemia
triglycerides
Online Access:https://www.mdpi.com/2227-9067/8/11/1078

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https://www.mdpi.com/2227-9067/8/11/1078

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