Unraveling rare form of adult-onset NIID by characteristic brain MRI features: A single-center retrospective review

Adult-onset neuronal intranuclear inclusion disease (NIID) is a rare neurodegenerative disorder with high clinical heterogeneity. Previous studies indicated that the high-intensity signals in the corticomedullary junction on diffusion-weighted imaging (DWI) on brain MRI, known as the “ribbon sign,”...

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Bibliographic Details
Main Authors: Fan Li, Qi Wang, Ying Zhu, Jiangxi Xiao, Muliang Gu, Jiaxi Yu, Jianwen Deng, Wei Sun, Zhaoxia Wang
Format: Article
Language:English
Published: Frontiers Media S.A. 2022-12-01
Series:Frontiers in Neurology
Subjects:
Online Access:https://www.frontiersin.org/articles/10.3389/fneur.2022.1085283/full