Angioedema due to acquired C1-inhibitor deficiency: spectrum and treatment with C1-inhibitor concentrate

Angioedema due to acquired C1-inhibitor deficiency: spectrum and treatment with C1-inhibitor concentrate

Abstract Background Acquired angioedema due to C1-inhibitor (C1-INH) deficiency (AAE-C1-INH) is a serious condition that may result in life-threatening asphyxiation due to laryngeal edema. It is associated with malignant B-cell lymphoma and other disorders. The purpose of this study was to describe...

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Bibliographic Details
Main Authors: Konrad Bork, Petra Staubach-Renz, Jochen Hardt
Format: Article
Language:English
Published: BMC 2019-03-01
Series:Orphanet Journal of Rare Diseases
Subjects:
Acquired angioedema
C1-inhibitor deficiency
Non-Hodgkin lymphoma
C1-inhibitor concentrate, C1-inhibitor antibodies
Online Access:http://link.springer.com/article/10.1186/s13023-019-1043-3

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http://link.springer.com/article/10.1186/s13023-019-1043-3

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