Non-functional alpha-cell hyperplasia with glucagon-producing NET: a case report

IntroductionAlpha-cell hyperplasia (ACH) is a rare pancreatic endocrine condition. Three types of ACH have been described: functional or nonglucagonoma hyperglucagonemic glucagonoma syndrome, reactive or secondary to defective glucagon signaling, and non-functional. Few cases of ACH with concomitant...

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Main Authors: Catarina Cidade-Rodrigues, Ana Paula Santos, Raquel Calheiros, Sara Santos, Catarina Matos, Ana Paula Moreira, Isabel Inácio, Pedro Souteiro, Joana Oliveira, Manuel Jácome, Sofia S. Pereira, Rui Henrique, Isabel Torres, Mariana P. Monteiro
Format: Article
Language:English
Published: Frontiers Media S.A. 2024-09-01
Series:Frontiers in Endocrinology
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Online Access:https://www.frontiersin.org/articles/10.3389/fendo.2024.1405835/full