Probability of sporadic lymphangioleiomyomatosis in women presenting with spontaneous pneumothorax

Probability of sporadic lymphangioleiomyomatosis in women presenting with spontaneous pneumothorax

Abstract Background Sporadic lymphangioleiomyomatosis (S-LAM) is a rare low-grade neoplasm of young women characterized by multiple pulmonary cysts leading to progressive dyspnea and recurrent spontaneous pneumothorax (SP). The diagnosis of S-LAM may be delayed by several years. To reduce this delay...

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Bibliographic Details
Main Authors: Audrey Suter, Marie-Eve Müller, Cécile Daccord, Patrick Taffé, Romain Lazor
Format: Article
Language:English
Published: BMC 2023-07-01
Series:Orphanet Journal of Rare Diseases
Subjects:
Lymphangioleiomyomatosis
Spontaneous pneumothorax
Primary spontaneous pneumothorax
Prevalence
Bayes theorem
Meta-analysis
Online Access:https://doi.org/10.1186/s13023-023-02784-5

Internet

https://doi.org/10.1186/s13023-023-02784-5

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