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  • TRANSTHYRETIN POLYNEUROPATHY (...
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TRANSTHYRETIN POLYNEUROPATHY (CLINICAL CASE)

TRANSTHYRETIN POLYNEUROPATHY (CLINICAL CASE)

Amyloidosis is a violation of protein metabolism, accompanied by the formation in tissues of a specific protein-polysaccharide complex (amyloid) of a fibrillar structure, characterized by a high orderliness of fibrils 5-10 nm thick due to the abundance of β-folded conformation in the secondary struc...

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Bibliographic Details
Main Authors: Наталья Викторовна Коробкова, Светлана Алексеевна Зуева, Ольга Валерьевна Рохленко, Вадим Гельевич Мозес, Елена Владимировна Рудаева, Светлана Ивановна Елгина, Кира Борисовна Мозес, Яэль Центер, Наталья Степановна Черных
Format: Article
Language:Russian
Published: The Publishing House Medicine and Enlightenment 2023-08-01
Series:Medicina v Kuzbasse
Subjects:
ген ttr
наследственный амилоидоз
полинейропатия
ттр-сап
транстиретин
Online Access:https://mednauki.ru/index.php/MK/article/view/955
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https://mednauki.ru/index.php/MK/article/view/955

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