ERDHEIM-CHESTER DISEASE (ECD): A RARE ETIOLOGY OF OBSTRUCTIVE ACUTE ABDOMEN IN A YOUNG PATIENT

Introduction: Erdheim-Chester disease (ECD) is a rare multisystemic disorder, classified as non-Langerhans histiocytosis according to WHO-2016. It is a malignant neoplasm derived from myeloid progenitor cells, particularly from monocytic/dendritic origin. Its actual incidence is unknown, and fewer t...

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Bibliographic Details
Main Authors: GGM Lima, PPF Machado, LF Castelo, V Rocha, LAPC Lage, J Pereira
Format: Article
Language:English
Published: Elsevier 2021-10-01
Series:Hematology, Transfusion and Cell Therapy
Online Access:http://www.sciencedirect.com/science/article/pii/S2531137921002686