2045 The role of TGFβ in driving early cystic fibrosis lung disease
OBJECTIVES/SPECIFIC AIMS: Transforming growth factor-beta (TGFβ) is a genetic modifier of cystic fibrosis (CF) lung disease. TGFβ’s pulmonary levels in young CF patients and its mechanism of action in CF are unknown. We examined TGFβ levels in children with CF and investigated responses of human air...
Main Authors: | Elizabeth L. Kramer, William Hardie, Kristin Hudock, Cynthia Davidson, Alicia Ostmann, John P. Clancy |
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格式: | Article |
語言: | English |
出版: |
Cambridge University Press
2018-06-01
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叢編: | Journal of Clinical and Translational Science |
在線閱讀: | https://www.cambridge.org/core/product/identifier/S2059866118001395/type/journal_article |
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