Cystic fibrosis modulator therapy can reverse cystic bronchiectasis

Abstract Bronchiectasis is often considered progressive and irreversible, so cases of regression or reversal are an important step in understanding the underlying pathophysiological mechanisms. Cystic fibrosis, (CF) caused by pathogenic variants in the cystic fibrosis transmembrane conductance regul...

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Bibliographic Details
Main Authors: Peter G. Middleton, Nicholas J. Simmonds
Format: Article
Language:English
Published: Wiley 2023-07-01
Series:Respirology Case Reports
Subjects:
Online Access:https://doi.org/10.1002/rcr2.1172