Acute Late-Onset Cirrhosis in Zellweger Spectrum Disorder
Zellweger spectrum disorders (ZSDs) are known to present with variable hepatic manifestations ranging from benign hepatosplenomegaly and elevated liver enzymes to advanced liver cirrhosis with hepatocellular carcinoma. However, the progression of liver disease in ZSD patients over time is poorly cha...
Main Authors: | , |
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Format: | Article |
Language: | English |
Published: |
Karger Publishers
2023-03-01
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Series: | Case Reports in Gastroenterology |
Subjects: | |
Online Access: | https://www.karger.com/Article/FullText/529353 |