Ketogenic diet treatment in adults with glycogenosis type IIIa (Morbus Cori)
Summary: Background: Glycogen storage disease type IIIa (GSDIIIa) is a defect of the debranching enzyme (amylo-1,6-glucosidase) in glycogenolysis and has an effect on the muscles and the liver. The guidelines for diagnosis and management of GSDIIIa primarily recommend a nutritional therapy to avoid...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Elsevier
2019-12-01
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| Series: | Clinical Nutrition Experimental |
| Online Access: | http://www.sciencedirect.com/science/article/pii/S235293931930123X |