Cranio-cervical decompression associated with non-instrumented occipito-C2 fusion in children with mucopolysaccharidoses: Report of twenty-one cases

Background: Mucopolysaccharidosis (MPS) is a multisystemic storage disorder of glycosaminoglycan deposits. Infiltration of the dura mater and supporting ligaments caused spinal cord compression and consecutive myelopathy, especially at the cranio-cervical junction (CCJ). Craniocervical instability a...

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Bibliographic Details
Main Authors: Mohamed Zairi, Ahmed Msakni, Ahmed Amin Mohseni, Nesrine Nessib, Sofiene Bouali, Rim Boussetta, Mohamed Nabil Nessib
Format: Article
Language:English
Published: Elsevier 2022-12-01
Series:North American Spine Society Journal
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2666548422000865