Hepatic fibrosis: a manifestation of the liver disease evolution in patients with Ataxia-telangiectasia

Hepatic fibrosis: a manifestation of the liver disease evolution in patients with Ataxia-telangiectasia

Abstract Background Ataxia-telangiectasia (A-T) is a DNA repair disorder characterized by changes in several organs and systems. Advances in clinical protocols have resulted in increased survival of A-T patients, however disease progression is evident, mainly through metabolic and liver changes. Obj...

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Bibliographic Details
Main Authors: Talita Lemos Neves Barreto, Roberto José de Carvalho Filho, David Carlos Shigueoka, Fernando Luiz Affonso Fonseca, Ariel Cordeiro Ferreira, Cristiane Kochi, Carolina Sanchez Aranda, Roseli Oselka Saccardo Sarni
Format: Article
Language:English
Published: BMC 2023-05-01
Series:Orphanet Journal of Rare Diseases
Subjects:
Ataxia-telangiectasia
Hepatic fibrosis
Image techniques by elasticity
Insulin resistance
Inflammation
Online Access:https://doi.org/10.1186/s13023-023-02720-7

Internet

https://doi.org/10.1186/s13023-023-02720-7

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