Hemophagocytic lymphohistiocytosis resulting from a cytokine storm triggered by septicemia in a child with chronic granuloma disease: a case report and literature review

Hemophagocytic lymphohistiocytosis resulting from a cytokine storm triggered by septicemia in a child with chronic granuloma disease: a case report and literature review

Abstract Background Hemophagocytic lymphohistiocytosis (HLH) is a rare potentially fatal illness characterized by impaired natural killer and cytotoxic T cell function. Chronic granulomatous disease (CGD) is an inherited immune deficiency caused by a defect in the nicotinamide adenine dinucleotide p...

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Bibliographic Details
Main Authors: Ang Wei, Honghao Ma, Liping Zhang, Zhigang Li, Qing Zhang, Dong Wang, Li Zhang, Hongyun Lian, Rui Zhang, Tianyou Wang
Format: Article
Language:English
Published: BMC 2020-03-01
Series:BMC Pediatrics
Subjects:
Chronic granuloma disease
Hemophagocytic Lymphohistiocytosis
Pathogenesis
Case report
IVIG
Online Access:http://link.springer.com/article/10.1186/s12887-020-1996-3

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http://link.springer.com/article/10.1186/s12887-020-1996-3

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