Pulmonary hypertension in hereditary hemorrhagic telangiectasia: A clinical review

Abstract Hereditary hemorrhagic telangiectasia (HHT) is a rare autosomal dominant hereditary disorder characterized by recurrent spontaneous epistaxis, mucocutaneous telangiectasias, and solid organ arteriovenous malformations (AVMs). Pulmonary hypertension (PH) is an increasingly recognized complic...

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Bibliographic Details
Main Authors: Akash Mathavan, Akshay Mathavan, Renuka Reddy, Kirk Jones, Christina Eagan, Hassan Alnuaimat, Ali Ataya
Format: Article
Language:English
Published: Wiley 2023-10-01
Series:Pulmonary Circulation
Subjects:
Online Access:https://doi.org/10.1002/pul2.12301