Establishment of a Bernard-Soulier syndrome model in zebrafish

Platelets play an essential role in thrombosis and hemostasis. Abnormal hemostasis can cause spontaneous or severe post-traumatic bleeding. Bernard-Soulier syndrome (BSS) is a rare inherited bleeding disorder caused by a complete quantitative deficiency in the GPIb-IX-V complex. Multiple mutations...

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Bibliographic Details
Main Authors: Qing Lin, Riyang Zhou, Panpan Meng, Liangliang Wu, Lian Yang, Wenyu Liu, Jiaye Wu, Yuhuan Cheng, Linjuan Shi, Yiyue Zhang
Format: Article
Language:English
Published: Ferrata Storti Foundation 2021-08-01
Series:Haematologica
Online Access:https://haematologica.org/article/view/10384