Intraoral and maxillofacial abnormalities in patients with autosomal dominant hyper-IgE syndrome
Autosomal dominant hyper-IgE syndrome (AD-HIES) is an inborn error of immunity (IEI) caused by a dominant-negative mutation in the signal transducer and activator of transcription 3 (STAT 3). This disease is characterized by chronic eczematoid dermatitis, recurrent staphylococcal skin abscesses, pne...
Main Authors: | , , , , , , , , , , , , , , , |
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Format: | Article |
Language: | English |
Published: |
Termedia Publishing House
2023-09-01
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Series: | Central European Journal of Immunology |
Subjects: | |
Online Access: | https://www.termedia.pl/Intraoral-and-maxillofacial-abnormalities-in-patients-with-autosomal-dominant-hyper-IgE-syndrome,10,51329,1,1.html |