Anesthesia management in living-donor liver transplantation in a patient with carbamoyl phosphate synthetase deficiency: a case report

Anesthesia management in living-donor liver transplantation in a patient with carbamoyl phosphate synthetase deficiency: a case report

Abstract Background Carbamoyl phosphate synthetase deficiency (CPS1D) is a urea-cycle disorder (UCD). We report successful perioperative management of pediatric living donor liver transplantation (LDLT) in a CPS1D patient. Case presentation A 10-year-old female patient with CPS1D underwent LDLT. Pro...

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Bibliographic Details
Main Authors: Hiroki Matsushita, Tetsushiro Fujiyoshi, Koichiro Yoshimaru, Toshiharu Matsuura, Yuichi Mushimoto, Yuji Karashima, Ken Yamaura
Format: Article
Language:English
Published: SpringerOpen 2022-09-01
Series:JA Clinical Reports
Subjects:
Pediatric
Urea cycle disorders
UCD
Carbamoyl phosphate synthetase deficiency
CPS1D
Hyperammonemia
Online Access:https://doi.org/10.1186/s40981-022-00558-9

Internet

https://doi.org/10.1186/s40981-022-00558-9

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