Hemophagocytic lymphohistiocytosis of indeterminate cause: a fatal adult case
Hemophagocytic lymphohistiocytosis (HLH) is an uncommon life-threatening disorder characterized by wide spread non-neoplastic proliferation and inappropriate activation of mature macrophages resulting in hypercytokinemia. This uncontrollable and ineffective systemic immune response causes fever, hep...
Main Authors: | , , , , , , |
---|---|
Format: | Article |
Language: | English |
Published: |
University of São Paulo
2012-06-01
|
Series: | Autopsy and Case Reports |
Subjects: | |
Online Access: | http://www.revistas.usp.br/autopsy/article/view/36457 |